Endogenous Lipoid Pneumonia in Adult Autoinflammatory Disease

We describe one of the first cases of endogenous lipoid pneumonia (ELP) in an adult patient with the clinical picture of adult‐onset Still disease (AOSD) and a low penetrance genetic background of tumor necrosis factor receptor‐associated periodic syndrome (TRAPS). This case highlights the complex pathophysiology of lung involvement in autoinflammatory diseases, operating at the interface of the innate and adaptive immune system.

• Publication year

  2025

• Venue

  Arthritis care & research

• Publication date

  2025-05-14

• Fields of study

  Medicine

• Identifiers
  DOI 10.1002/acr.25570PMID 40368851
• External record

  Open on Semantic Scholar

• Source metadata

  Semantic Scholar, PubMed

• No claims are published for this paper.

• No concepts are published for this paper.

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