Lymphoproliferative disease and acquired C1 inhibitor deficiency.

Angioedema due to acquired deficiency of the C1-inhibitor is a bridging condition between autoimmunity and lymphoproliferation. We report 32 patients with acquired C1 inhibitor deficiency: 23 have anti C1-inhibitor autoantibodies; 13 have monoclonal gammopathies of unknown significance and 9 have non-Hodgkin's lymphoma. Our series suggest that different forms of B cell disorders coexist and/or evolve into each other in acquired angioedema.

• Publication year

  2007

• Venue

  Haematologica

• Publication date

  2007-05-01

• Fields of study

  Medicine

• Identifiers
  DOI 10.3324/HAEMATOL.10769PMID 17488706
• External record

  Open on Semantic Scholar

• Source metadata

  Semantic Scholar, PubMed

• No claims are published for this paper.

• No concepts are published for this paper.

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