Orotic acid in urine and hyperammonemia.

No abstract is available for this paper.

• Publication year

  1982

• Venue

  Advances in Experimental Medicine and Biology

• Publication date

  Unknown publication date

• Fields of study

  Medicine, Chemistry

• Identifiers
  DOI 10.1007/978-1-4757-6903-6_38PMID 7164906
• External record

  Open on Semantic Scholar

• Source metadata

  Semantic Scholar, PubMed

• No claims are published for this paper.

• No concepts are published for this paper.

• Haptoglobin types and subtypes in Alzheimer's disease and senile dementia

  2004cited by this paper
• Pyrimidine and purine metabolites in ornithine carbamoyl transferase deficiency

  1981cited by this paper
• Effect of ammonium ion on pyrimidine synthesis de novo in isolated rat hepatocytes.

  1981cited by this paper
• Determination of Orotic Acid in Children’s Urine

  1980cited by this paper
• Failure of the normal ureagenic response to amino acids in organic acid-loaded rats. Proposed mechanism for the hyperammonemia of propionic and methylmalonic acidemia.

  1980cited by this paper
• Urinary purines and pyrimidines in patients with hyperammonemia of various origins.

  1980cited by this paper
• Diagnostic value of orotic acid excretion in heritable disorders of the urea cycle and in hyperammonemia due to organic acidurias

  1980cited by this paper
• Purine and pyrimidine metabolism in hereditary orotic aciduria: some unexpected effects of allopurinol

  1980cited by this paper
• Hepatic ornithine aminotransferase in the rat after portacaval shunt.

  1980cited by this paper
• Inhibition by propionyl-coenzyme A of N-acetylglutamate synthetase in rat liver mitochondria. A possible explanation for hyperammonemia in propionic and methylmalonic acidemia.

  1979cited by this paper
• Orotic acid biosynthesis in arginine-deficient rats.

  1979cited by this paper
• Effect of propionate and pyruvate on citrulline synthesis and ATP content in rat liver mitochondria.

  1979cited by this paper
• Interrelationships between gluconeogenesis and ureogenesis in isolated hepatocytes.

  1978cited by this paper
• Orotic acid biosynthesis in rat liver: studies on the source of carbamoylphosphate.

  1977cited by this paper
• HEREDITARY ORNITHINE TRANSCARBAMYLASE DEFICIENCY

  1975cited by this paper
• Determination of orotic and dihydroorotic acids in biological fluids and tissues.

  1975cited by this paper
• Aggregation states and catalytic properties of the multienzyme complex catalyzing the initial steps of pyrimidine biosynthesis in rat liver.

  1975cited by this paper
• A case of carbamyl phosphate synthetase deficiency.

  1972cited by this paper
• Enzymatic synthesis of acetylglutamate by mammalian liver preparations and its stimulation by arginine.

  1971cited by this paper
• On the availability of intramitochondrial carbamoylphosphate for the extramitochondrial biosynthesis of pyrimidines.

  1969cited by this paper
• Control of pyrimidine biosynthesis in mammalian tissues. I. Partial purification and characterization of glutamine-utilizing carbamyl phosphate synthetase of mouse spleen and its tissue distribution.

  1969cited by this paper
• Hyperammonaemia. A new instance of an inborn enzymatic defect of the biosynthesis of urea.

  1962cited by this paper

• Acute and sub-acute oral toxicological evaluations and mutagenicity of N-carbamylglutamate (NCG).

  2015cites this paper
• Hyperargininemia due to arginase I deficiency: the original patients and their natural history, and a review of the literature

  2015cites this paper
• Current role of enzyme analysis for urea cycle disorders

  2014cites this paper
• Potential role of N-carbamoyl glutamate in biosynthesis of arginine and its significance in production of ruminant animals

  2013cites this paper
• Suggested guidelines for the diagnosis and management of urea cycle disorders

  2012cites this paper
• N-Carbamylglutamate Enhances Pregnancy Outcome in Rats through Activation of the PI3K/PKB/mTOR Signaling Pathway

  2012cites this paper
• N-Carbamylglutamate protects patients with decompensated propionicaciduria from hyperammonaemia

  2005cites this paper
• Carrier detection in a partially dominant X-linked disease: ornithine transcarbamylase deficiency

  2004cites this paper
• Liver pathology in a new congenital disorder of urea synthesis: N-acetylglutamate synthetase deficiency

  2004cites this paper
• N-carbamylglutamate enhances ammonia detoxification in a patient with decompensated methylmalonic aciduria.

  2003cites this paper
• Ornithine transcarbamylase (OTC) deficiency in a female patient with a de novo deletion of the paternal X chromosome

  1992cites this paper
• Orotic aciduria due to arginine deprivation: changes in the levels of carbamoyl phosphate and of other urea cycle intermediates in mouse liver.

  1989cites this paper
• DNA analysis of ornithine transcarbamylase deficiency

  1988cites this paper
• Diagnosis of urea cycle disorders.

  1987cites this paper
• Risk of serious illness in heterozygotes for ornithine transcarbamylase deficiency.

  1986cites this paper
• Treatment of congenital hyperammonemias.

  1984cites this paper