Extra-Abdominal Desmoid Tumours: A Review of the Literature

Extra-abdominal desmoid lesions, otherwise known as aggressive fibromatosis, are slow-growing benign lesions which may be encountered in clinical practice. Recent controversies exist regarding their optimal treatment. Given their benign nature, is major debulking surgery justified, or is it worth administering chemotherapy for a disease process which unusually defies common teaching and responds to such medications? We present a literature review of this particular pathology discussing the aetiology, clinical presentation, and various current controversies in the treatment options.

• Publication year

  2012

• Venue

  Sarcoma

• Publication date

  2012-08-16

• Fields of study

  Medicine

• Identifiers
  DOI 10.1155/2012/578052PMID 22966217PMCID 3431123
• External record

  Open on Semantic Scholar

• Source metadata

  Semantic Scholar, PubMed

• No claims are published for this paper.

• No concepts are published for this paper.

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