Evidence for accessory pathway of galactose metabolism in mammalian liver.

No abstract is available for this paper.

• Publication year

  1957

• Venue

  Science

• Publication date

  1957-10-04

• Fields of study

  Biology, Medicine, Chemistry

• Identifiers
  DOI 10.1126/SCIENCE.126.3275.652-APMID 13467261
• External record

  Open on Semantic Scholar

• Source metadata

  Semantic Scholar, PubMed

• No claims are published for this paper.

• No concepts are published for this paper.

• Formation and interconversion of sugar nucleotides by plant extracts.

  1957cited by this paper
• Defect in uptake of galactose-1-phosphate into liver nucleotides in congenital galactosemia.

  1957cited by this paper
• Studies on metabolism of carbon-14-labeled galactose in a galactosemic individual.

  1957cited by this paper
• Galactosemia, a congenital defect in a nucleotide transferase.

  1956cited by this paper
• Congenital galactosemia, a single enzymatic block in galactose metabolism.

  1956cited by this paper
• Uridine compounds in glucuronic acid metabolism. I. The formation of glucuronides in liver suspensions.

  1954cited by this paper
• Uridyl Transferases and the Formation of Uridine Triphosphate : Uridyl Transferases and the Formation of Uridine Diphosphogalactose

  1953cited by this paper
• Studies on uridine-diphosphate-glucose.

  1952cited by this paper
• Galactosemia and its relation to Laennec's cirrhosis; review of the literature and presentation of six additional cases.

  1951cited by this paper
• Amino acids of two insect viruses.

  1951cited by this paper
• The Threshold for Sudden Changes in the Velocity of a Seen Object

  1950cited by this paper

• Restoring galactose metabolism without restoring GALT rescues both compromised survival in larvae and an adult climbing deficit in a GALT‐null D. Melanogaster model of classic galactosemia

  2024cites this paper
• Defects in Galactose Metabolism and Glycoconjugate Biosynthesis in a UDP-Glucose Pyrophosphorylase-Deficient Cell Line Are Reversed by Adding Galactose to the Growth Medium

  2020cites this paper
• Galactose‐1‐phosphate uridyltransferase deficiency: A literature review of the putative mechanisms of short and long‐term complications and allelic variants

  2018cites this paper
• Transient activity in monkey area MT represents speed changes and is correlated with human behavioral performance.

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• Testing Bayesian and heuristic predictions of mass judgments of colliding objects

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• Base on balls for the Chapman strategy: Reassessing Brouwer, Brenner, and Smeets (2002)

  2012cites this paper
• Biosynthesis of Galactofuranose in Kinetoplastids: Novel Therapeutic Targets for Treating Leishmaniasis and Chagas' Disease

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• Control of Rate of Intracellular Respiration

  2008cites this paper
• Biochemical Genetics as Illustrated by Hereditary Galactosaemia

  2008cites this paper
• Rôle of Uridine Diphosphate Glucose in the Synthesis of Glycogen

  2008cites this paper
• DRUG-INDUCED HEMOLYTIC ANEMIAS AND CONGENITAL GALACTOSEITIA*

  2007cites this paper
• Classical galactosaemia revisited

  2006cites this paper
• Mediators of Galactose Sensitivity in UDP-Galactose 4′-Epimerase-impaired Mammalian Cells*

  2005cites this paper
• Effects of galactosemia in utero

  2005influential citation
• Differential roles of the Leloir pathway enzymes and metabolites in defining galactose sensitivity in yeast.

  2004cites this paper
• Renal excretion of galactose and galactitol in patients with classical galactosaemia, obligate heterozygous parents and healthy subjects

  2003cites this paper
• Overexpression of human UDP-glucose pyrophosphorylase rescues galactose-1-phosphate uridyltransferase-deficient yeast.

  2000cites this paper
• Expression of human inositol monophosphatase suppresses galactose toxicity in Saccharomyces cerevisiae: possible implications in galactosemia.

  1999cites this paper
• Inborn Errors of Carbohydrate Metabolism

  1998cites this paper
• A Search for Transferase Galactosemia Genes in the South African Negroid Population

  1998cites this paper
• Inherited disorders of galactose metabolism and cultured cells

  1994cites this paper
• Clinical and biochemical evidence of skeletal muscle involvement in galactose-1-phosphate uridyl transferase deficiency

  1993cites this paper
• A Study of Galactose Intolerance in Human and Rat Liver In Vivo by 31P Magnetic Resonance Spectroscopy

  1992cites this paper
• 31P MR Spectroscopic Studies of Metabolic Lesions in the Liver

  1992cites this paper
• Agarose gel isoelectrofocusing of UDP-galactose pyrophosphorylase and galactose-1-phosphate uridyltransferase. Developmental aspect of UDP-galactose pyrophosphorylase.

  1987cites this paper
• Nutritional Significance of Lactose: II. Metabolism and Toxicity of Galactose

  1985cites this paper
• Whole-body autoradiographic study on the distribution of (U-14C)galactose in adult, pregnant, newborn and infant mice.

  1984cites this paper
• Isolation and synthesis of sugar nucleotides.

  1982cites this paper
• Galactosaemia — thirty years on. the experience of a generation

  1982cites this paper
• Metabolic effects of dietary galactose.

  1982cites this paper
• Galactose intolerance in individuals with double heterozygosity for Duarte variant and galactosemia.

  1982cites this paper
• [27] Isolation and synthesis of sugar nucleotides

  1982cites this paper
• Galactose metabolism, hereditary defects and their clinical significance

  1980cites this paper
• Galactose oxidation in liver.

  1979cites this paper
• Impaired adaptation to extrauterine life: a teratogenic event

  1979cites this paper
• Galactose-1-phosphate uridylyltransferase activity in chronic lymphocytic leukemia.

  1979cites this paper
• Biochemical expression of the galactosemic defect in lymphocytes and the effects on glycoprotein synthesis.

  1977cites this paper
• The effect of pH on incorporation of galactose by a normal human cell line and cell lines from patients with defective galactose metabolism

  1976cites this paper
• Galactose and glucose metabolism in galactokinase deficient, galactose‐1‐P‐uridyl transferase deficient and normal human fibroblasts

  1975cites this paper
• Studies on the metabolism of galactose-6-phosphate in rat heart and brain.

  1975cites this paper
• Effects of menadione on the metabolism of galactose in regenerating rat liver.

  1974cites this paper
• Effects of menadione on the metabolism of galactose in regenerating rat liver.

  1974cites this paper
• UDP-galactose:glycoprotein galactosyltransferase activity in tissues of developing rat.

  1974cites this paper
• Detection of Inborn Errors of Metabolism: Galactosemia

  1973cites this paper
• 2 Uridine Diphosphoryl Glucose Pyrophosphorylase

  1973cites this paper
• Galactose Utilization in Galactosemia

  1972cites this paper
• Plasma insulin and growth hormone in galactosemia.

  1972cites this paper
• Galactose metabolism of the red cell.

  1971cites this paper
• Developmental changes in the activity of galactose-1-phosphate uridylyltransferase in the rat.

  1971cites this paper
• Perception of Changes in Certain Exteroceptive Stimuli

  1971cites this paper
• Liver galactose-1-phosphate uridyl transferase: activity in normal and galactosemic subjects.

  1971cites this paper
• CHAPTER 2 – The Developmental Formation of Enzymes in Rat Liver

  1970cites this paper
• Uridine diphosphate glucose pyrophosphorylase. IV. Crystallization and properties of the enzyme from human liver.

  1970cites this paper
• Hormonal control of fetal development and metabolism.

  1970cites this paper
• The inherited defects of erythrocyte metabolism.

  1969cites this paper
• Erythrocyte galactose-1-phosphate uridyl transferase activity in infants of low birth weight.

  1969cites this paper
• Human hepatic uridine diphosphate galactose pyrophosphorylase. Its characterization and activity during development.

  1969cites this paper
• Epimerase-catalyzed glucose-galactose interconversion in the developing mouse brain.

  1969cites this paper
• Galactosemia.

  1968cites this paper
• The galactose metabolic pathway.

  1968cites this paper
• The oxidation of C14galactose by patients with congenital galactosemia: Evidence for a direct oxidative pathway

  1968cites this paper
• Galactosemia in a 24-year-old man; detection by enzyme studies.

  1968cites this paper
• Cataracts and galactose metabolism.

  1967cites this paper
• Other Pathways of Carbohydrate Metabolism

  1967cites this paper
• Glucose-1-phosphate uridylyl transferase activity in developing rat liver.

  1966cites this paper
• Biochemical and genetic aspects of mental retardation.

  1966cites this paper
• Developmental aspects and some characteristics of mammalian galactose 1-phosphate uridyltransferase.

  1966cites this paper
• Biochemical aspects of developing function in newborn mammalian liver.

  1966cites this paper
• UDPG-4-epimerase activity in human fibroblasts in cell culture

  1966cites this paper
• Galactose Conversion to d-Xylulose: An Alternate Route of Galactose Metabolism

  1966cites this paper
• Mammalian galactose dehydrogenase. II. Properties, substrate specificity, and developmental changes.

  1966cites this paper
• Bestimmung der Galaktose-1-Phosphat-Uridyltransferase im Capillarblut bei der Galaktosämie

  1965cites this paper
• [Determination of galactose-1-phosphate uridyl transferase in capillary blood in galactosemia. Use in family examinations].

  1965cites this paper
• MAMMALIAN GALACTOKINASE. DEVELOPMENTAL AND ADAPTIVE CHARACTERISTICS IN THE RAT LIVER.

  1965cites this paper
• Experimental studies on the leukemogenesis in mice

  1965cites this paper
• THE METABOLISM OF GALACTOSE BY PATIENTS WITH CONGENITAL GALACTOSEMIA.

  1965cites this paper
• Unexpected Acute Toxicity of Aminopterin

  1964cites this paper
• THE ISOLATION AND IDENTIFICATION OF GALACTITOL FROM THE URINE OF PATIENTS WITH GALACTOSEMIA.

  1964cites this paper
• GALACTOSEMIA AND NUTRITION.

  1964cites this paper
• SUGAR NUCLEOTIDES AND THE SYNTHESIS OF CARBOHYDRATES.

  1964cites this paper
• CARCINOGENESIS STUDY WITH DIMETHYLNITROSAMINE ADMINISTERED ORALLY TO ADULT AND SUBCUTANEOUSLY TO NEWBORN BALB-C MICE.

  1964cites this paper
• Galactose-1-Phosphate Uridyl Transferase Activity in Galactosæmia

  1964cites this paper
• GLYCOGEN SYNTHESIS AND BREAKDOWN IN FETAL AND NEWBORN RAT LIVER

  1963cites this paper
• Glycogen synthesis and breakdown in rat liver at birth.

  1963cites this paper
• Inherited Metabolic Disorders: Galactosemia

  1963cites this paper
• Observations on cataract formation in the newborn offspring of rats fed a high-galactose diet.

  1963cites this paper
• CHAPTER 2 – THE BIOGENESIS OF PURINE AND PYRIMIDINE NUCLEOTIDES

  1963cites this paper
• BIOSYNTHESIS OF SACCHARIDES FROM GLYCOPYRANOSYL ESTERS OF NUCLEOTIDES ("SUGAR NUCLEOTIDES").

  1963cites this paper
• Measurement of UDP-enzyme systems.

  1962cites this paper
• Biochemical Genetics and Mental Retardation.

  1962cites this paper
• [Nucleotides of the central nervous system].

  1962cites this paper
• Diet in relation to hereditary metabolic disorders.

  1962cites this paper
• Pathways of Metabolism in Nucleate and Anucleate Erythrocytes

  1962cites this paper
• Beneficial effect of orotic acid upon galactose metabolism of erythrocytes from congenital galactosemia.

  1962cites this paper
• Galactosemia: clinical, genetic, and biochemical study.

  1961cites this paper
• Galactosemia. A family study.

  1961cites this paper
• [On the biochemical genetics of galactosemia].

  1961cites this paper
• Galactosemia: clinical, genetic, and biochemical study.

  1961cites this paper
• Biochemical genetics as illustrated by hereditary galactosemia.

  1961cites this paper
• SOME OBSERVATIONS ON THE METABOLISM OF D-GALACTOSE IN NORMAL MAN.

  1961cites this paper