A prolidase deficiency in man with iminopeptiduria.

No abstract is available for this paper.

• Publication year

  1974

• Venue

  Metabolism: Clinical and Experimental

• Publication date

  1974-06-01

• Fields of study

  Biology, Medicine

• Identifiers
  DOI 10.1016/0026-0495(74)90078-XPMID 4828441
• External record

  Open on Semantic Scholar

• Source metadata

  Semantic Scholar, PubMed

• No claims are published for this paper.

• No concepts are published for this paper.

• Letter: Intravenous regional sympathetic block with guanethidine.

  1974cited by this paper
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  1972cited by this paper
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  1972cited by this paper
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  1970cited by this paper
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  1970cited by this paper
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  1970cited by this paper
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  1970cited by this paper
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  1969cited by this paper
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  1969cited by this paper
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  1968cited by this paper
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  1967cited by this paper
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  1967cited by this paper
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  1966cited by this paper
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  1965cited by this paper
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  1965cited by this paper
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  1965cited by this paper
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  1964cited by this paper
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  1964cited by this paper
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  1963cited by this paper
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  1960cited by this paper
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  1955cited by this paper
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  1955cited by this paper
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  1954cited by this paper
• The amino-acids and other ampholytes of urine. 1. A general method of isolation

  1952cited by this paper
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  1952cited by this paper
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  1952cited by this paper

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  2025cites this paper
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  2023cites this paper
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  2023cites this paper
• Quantitative analysis of the natural history of prolidase deficiency: description of 17 families and systematic review of published cases

  2021cites this paper
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  2017cites this paper
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  2017cites this paper
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  2017cites this paper
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  2016cites this paper
• Massive splenomegaly secondary to prolidase deficiency.

  2015cites this paper
• Prolidase Is Required for Early Trafficking Events during Influenza A Virus Entry

  2014cites this paper
• Prolidase deficiency: dento-facial aspects in a paediatric patient.

  2014cites this paper
• Xaa-Pro Dipeptidase (Eukaryotes)

  2013cites this paper
• Obesity, genetics and the skin

  2013cites this paper
• Prolidase deficiency breaks tolerance to lupus‐associated antigens

  2013cites this paper
• Structure-function relationship study of a loop structure in allosteric behaviour and substrate inhibition of Lactococcus lactis prolidase

  2011cites this paper
• Charged residues on a flap-loop structure of Lactococcus lactis prolidase play critical roles in allosteric behavior and substrate inhibition.

  2011cites this paper
• Prolidase activity dysregulation and its correlation with oxidative–antioxidative status in chronic obstructive pulmonary disease

  2011cites this paper
• Prolidase Deficiency: A child with persistent lower extremity ulcerations

  2011cites this paper
• Prolidase deficiency: a rare aetiology of arthritis.

  2010cites this paper
• An Amish boy with recurrent ulcerations of the lower extremities, telangiectases of the hands, and chronic lung disease.

  2010cites this paper
• Prolidase deficiency: it looks like systemic lupus erythematosus but it is not

  2010cites this paper
• Le déficit en prolidase: une cause rare de polyarthrite

  2010cites this paper
• Positional cloning of adiposity genes in ethnic minorities of the Insulin Resistance Atherosclerosis Family Study

  2009cites this paper
• Activity of prolidase isoenzymes in the rat brain: subcellular and regional distribution during development.

  2009cites this paper
• Characterization of prolidase I and II purified from normal human erythrocytes: comparison with prolidase in erythrocytes from a patient with prolidase deficiency

  2009cites this paper
• CHAPTER 72 – Amino Acids, Oligopeptides, and Hyperaminoacidurias

  2008cites this paper
• Nasal reconstruction in a patient with prolidase deficiency syndrome.

  2008cites this paper
• Different effects of sulfur amino acids on prolidase and prolinase activity in normal and prolidase-deficient human erythrocytes.

  2007cites this paper
• Optimization of the Photometric Enzyme Activity Assay For Evaluating Real Activity of Prolidase ]

  2007cites this paper
• Prolidase Isoenzymes in the Rat: Their Organ Distribution, Developmental Change and Specific Inhibitors

  2007cites this paper
• A nonsense mutation of PEPD in four Amish children with prolidase deficiency

  2006cites this paper
• Prolidase deficiency and the biochemical assays used in its diagnosis.

  2006cites this paper
• The role of emerging techniques in the investigation of prolidase deficiency: from diagnosis to the development of a possible therapeutical approach.

  2006cites this paper
• Characterization of prolidase activity in erythrocytes from a patient with prolidase deficiency: comparison with prolidase I and II purified from normal human erythrocytes.

  2005cites this paper
• Characteristics of prolinase against various iminodipeptides in erythrocyte lysates from a normal human and a patient with prolidase deficiency

  2004cites this paper
• Determination of prolidase activity using matrix-assisted laser desorption/ionization time-of-flight mass spectrometry.

  2004cites this paper
• Effects of amino acids and its metabolites on prolidase activity against various iminodipeptides in erythrocytes from normal human and a patient with prolidase deficiency.

  2004cites this paper
• An autopsy case of prolidase deficiency

  2004cites this paper
• Characteristics of Prolidase from the Erythrocytes of Normal Humans and Patients with Prolidase Deficiency and Their Mother

  2003cites this paper
• Prolidase deficiency

  2002cites this paper
• Corticosteroid treatment of prolidase deficiency skin lesions by inhibiting iminodipeptide‐primed neutrophil superoxide generation

  1999cites this paper
• The effects of serum iminodipeptides and prednisolone on superoxide generation and tyrosyl phosphorylation of proteins in neutrophils from a patient with prolidase deficiency.

  1998cites this paper
• Prolidase deficiency associated with pathologic myopia.

  1998cites this paper
• Direct monitoring of prolidase activity in cultured skin fibroblasts using capillary electrophoresis.

  1997cites this paper
• Analyses of iminodipeptides containing C-terminal proline or hydroxyproline in biological samples by liquid chromatography/mass spectrometry

  1997cites this paper
• Erythrocyte L-aspartyl-L-phenylalanine hydrolase activity and plasma phenylalanine and aspartate concentrations in children consuming diets high in aspartame.

  1995cites this paper
• Idiopathic thrombocytopenia and neutropenia in childhood.

  1994cites this paper
• Measurement of Iminodipeptides in the Serum of Patients with Prolidase Deficiency Using Liquid Chromatography-Mass Spectrometry

  1994cites this paper
• Iminodipeptides containing proline with C-terminal and N-terminal residues prime the stimulation of human neutrophil superoxide generation by fMLP.

  1994cites this paper
• Prolidase deficiency: a multisystemic hereditary disorder.

  1993cites this paper
• The Use of Liquid Chromatography-Mass Spectrometry for the Identification and Quantification of Urinary Iminodipeptides in Prolidase Deficiency

  1993cites this paper
• Increased excretion of proline-containing peptides in dipeptidyl peptidase IV-deficient rats.

  1993cites this paper
• Liquid chromatography-mass spectrometry for simultaneous analyses of iminodipeptides containing an N-terminal or a C-terminal proline.

  1991cites this paper
• Ultrastructural studies on dermis from prolidase deficient subjects.

  1991cites this paper
• Tubular Transport of Amino Acids and Small Peptides

  1991cites this paper
• A catalogue of multiple congenital anomaly syndromes

  1991cites this paper
• Molecular basis of prolidase (peptidase D) deficiency.

  1991cites this paper
• Characterization of prolidase I and II from erythrocytes of a control, a patient with prolidase deficiency and her mother.

  1990cites this paper
• Biochemical basis of prolidase deficiency. Polypeptide and RNA phenotypes and the relation to clinical phenotypes.

  1990cites this paper
• High-performance liquid chromatographic procedure for the determination of serum prolidase activity.

  1990cites this paper
• Liquid chromatography-mass spectrometry for the qualitative analyses of iminodipeptides in the urine of patients with prolidase deficiency.

  1990cites this paper
• Genetic Defects of the Metabolism of Magnesium, Zinc, Manganese, Molybdenum, and Selenium

  1990cites this paper
• Characteristics and partial purification of prolidase and prolinase from leukocytes of a normal human and a patient with prolidase deficiency.

  1989cites this paper
• Separation of two erythrocyte prolidase isoforms by fast protein liquid chromatography; application to prolidase deficiency.

  1989cites this paper
• Prolidase deficiency: a case report and literature review

  1989cites this paper
• The renal handling of amino acids and oligopeptides.

  1988cites this paper
• Characteristics of Partially Purified Prolidase from Erythrocytes of Normal Individuals, of Two Patients with Prolidase Deficiency, and of the Patients' Mother

  1988cites this paper
• Immunochemical Analyses of Prolidase Deficiency Sera

  1988cites this paper
• Biochemical investigations on prolidase and prolinase in erythrocytes from patients with prolidase deficiency.

  1988cites this paper
• Prolidase deficiency: A patient without hydroxyproline-containing iminodipeptides in urine

  1988cites this paper
• Biochemical studies on prolidase in sera from control, patients with prolidase deficiency and their mother

  1988cites this paper
• Characteristics of Prolidase and Prolinase in Prolidase‐deficient Patients with Some Preliminary Studies of Their Role in Skin

  1988cites this paper
• Prolidase deficiency in two siblings with chronic leg ulcerations. Clinical, biochemical, and morphologic aspects.

  1987cites this paper
• Increased manganese content and reduced arginase activity in erythrocytes of a patient with prolidase deficiency (iminodipeptiduria)

  1986cites this paper
• Intestinal hydrolysis of aspartylphenylalanine--the metabolic product of aspartame.

  1986cites this paper
• Direct NMR evidence that prolidase is specific for the trans isomer of imidodipeptide substrates.

  1986cites this paper
• Simultaneous measurement of prolidase and prolinase activities in erythrocytes using an isotachophoretic analyser.

  1985cites this paper
• Metabolism of glycine- and hydroxyproline-containing peptides by the isolated perfused rat kidney.

  1985cites this paper
• Possible involvement of aminopeptidase, an ecto-enzyme, in the inactivation of bradykinin by intact neutrophils.

  1985cites this paper
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  1985cites this paper
• Simultaneous measurement of prolidase and prolinase activities in erythrocytes using an isotachophoretic analyser.

  1985cites this paper
• Congenital Expression of Prolidase Defect in Prolidase Deficiency

  1984cites this paper
• Substrate Specificity Prolidase in Control Skin Fibroblasts of Manganese-activated and Prolidase-deficient Cultured

  1984cites this paper
• Prolidase deficiency: characteristics of human skin fibroblast prolidase using colorimetric and fluorimetric assays.

  1984cites this paper
• Isotachophoretic analysis of iminopeptides in the urine of patients with iminopeptiduria.

  1984cites this paper
• Substrate specificity of manganese-activated prolidase in control and prolidase-deficient cultured skin fibroblasts

  1984cites this paper
• Clinical and biochemical characteristics of prolidase deficiency in siblings.

  1984cites this paper
• Effect of Different Total Parenteral Nutrition Fuel Mixes on the Body Composition of Infant Miniature Pigs

  1984cites this paper
• Pathogenesis of ulcerations in deficiency of prolidase. The role of angiopathy and of deposits of amyloid.

  1984cites this paper
• Prolidase and prolidase deficiency.

  1984cites this paper
• Measurement of prolidase activity in erythrocytes using isotachophoresis.

  1984cites this paper
• Amino acid metabolism by the kidney.

  1983cites this paper
• PROLIDASE DEFICIENCY

  1983cites this paper
• In-vitro responses to ascorbate and manganese in fibroblasts from a patient with prolidase deficiency and iminodipeptiduria: Cell growth, prolidase activity and collagen metabolism

  1983influential citation
• Fluorimetric assay for prolinase and partial characterisation in cultured skin fibroblasts.

  1982cites this paper