PFAPA syndrome.

No abstract is available for this paper.

• Publication year

  1989

• Venue

  The Pediatric Infectious Disease Journal

• Publication date

  Unknown publication date

• Fields of study

  Medicine

• Identifiers
  DOI 10.1097/00006454-198909000-00026PMID 2797967
• External record

  Open on Semantic Scholar

• Source metadata

  Semantic Scholar, PubMed

• No claims are published for this paper.

• No concepts are published for this paper.

• Periodic fever associated with aphthous stomatitis, pharyngitis and cervical adenitis.

  1989cited by this paper
• Possible role of tonsillectomy and adenoidectomy in children with recurrent fever and tonsillopharyngitis.

  1989cited by this paper
• Syndrome of periodic fever, pharyngitis, and aphthous stomatitis.

  1987cited by this paper
• Syndrome of periodic fever and pharyngitis.

  1987cited by this paper
• Behçet syndrome.

  1985cited by this paper
• Hyperimmunoglobulinaemia D and periodic fever: a new syndrome.

  1984cited by this paper
• Human Cyclic Neutropenia: Clinical Review and Long-Term Follow-up of Patients

  1981cited by this paper
• Familial Mediterranean fever. A survey of 470 cases and review of the literature.

  1967cited by this paper

• Pediatric Systemic Autoinflammatory Disorders: An Overview

  2025cites this paper
• Neglected adult PFAPA syndrome

  2025influential citation
• Features Associated with Response to Tonsillectomy in Periodic Fever, Aphthous Stomatitis, Pharyngitis, and Cervical Adenitis Syndrome in Children.

  2025cites this paper
• Inflammatory turmoil within: an exploration of autoinflammatory disease genetic underpinnings, clinical presentations, and therapeutic approaches

  2024cites this paper
• Autoinflammatory Diseases: A Review

  2024cites this paper
• Periodic Fever, Aphthous Stomatitis, Pharyngitis, and Adenitis (PFAPA) Syndrome: An Overview for Primary Care Practitioners

  2024cites this paper
• Exploring the immunological basis of periodic fever, aphthous stomatitis, pharyngitis, and adenitis (PFAPA) syndrome: immunohistochemical staining features of palatine tonsils

  2023cites this paper
• The use of ketotifen as long-term anti-inflammatory prophylaxis in children with PFAPA syndrome

  2023cites this paper
• Periodic Fever in Children: A Report of Three Unusual Cases

  2023cites this paper
• What is PFAPA syndrome? Genetic clues about the pathogenesis

  2023cites this paper
• Diagnostic performance of routine blood parameters in periodic fever, aphthous stomatitis, pharyngitis, and adenitis syndrome

  2023cites this paper
• PFAPA syndrome: A practical review

  2022cites this paper
• An autoinflammatory disease – PFAPA syndrome: a single-center experience

  2022cites this paper
• Epidemiology and clinical features of PFAPA: a retrospective cohort study of 336 patients in western Sweden

  2022cites this paper
• Long-term efficacy of tonsillectomy/adenotonsillectomy in patients with periodic fever aphthous stomatitis pharyngitis adenitis syndrome with special emphasis on co-existence of familial Mediterranean fever

  2022cites this paper
• Challenges in the diagnosis of periodic fever, aphthous stomatitis, pharyngitis, and adenitis syndrome in developing countries—A decade of experience from North India

  2022cites this paper
• Tonsil Mycobiome in PFAPA (Periodic Fever, Aphthous Stomatitis, Pharyngitis, Adenitis) Syndrome: A Case-Control Study

  2021cites this paper
• Vestibular involvement of PFAPA syndrome.

  2021cites this paper
• Clinical Usefulness of Acute-Phase Markers in Distinguishing between PFAPA and Other Exudative Tonsillitis Causes: A Methodological Study.

  2021cites this paper
• What is hiden behind autoinflammation?

  2020cites this paper
• Long-term management of patients with PFAPA syndrome

  2020cites this paper
• Characteristics and Disease Course in a Cohort of Children With PFAPA Syndrome in the Community of Madrid, Spain

  2019cites this paper
• Towards better diagnostic criteria for periodic fever, aphthous stomatitis, pharyngitis and adenitis syndrome

  2019cites this paper
• Results of surgical treatment of children with PFAPA syndrome

  2019cites this paper
• Periodic and Non-Periodic Fevers

  2019cites this paper
• Tonsillectomy for periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis syndrome (PFAPA).

  2019cites this paper
• PFAPA: Periodic Fever, Aphthous Ulceration, Pharyngitis, Adenitis

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• Recurrent Fever and Sore Throat

  2019cites this paper
• Pediatric Rheumatology for Adult Rheumatologists

  2019cites this paper
• Evaluation of co-existing diseases in children with familial Mediterranean fever

  2019cites this paper
• Clinical features and new diagnostic criteria for the syndrome of periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis

  2019cites this paper
• Síndrome PFAPA: Diagnóstico e Tratamento na Atenção Primária à Saúde

  2019cites this paper
• Remarkable effectiveness of tocilizumab in familial Mediterranean fever exon 3 variant with severe abdominal pain and PFAPA-like symptoms: a child case report and review of the literature

  2019cites this paper
• From uncertainty to gradually managing and awaiting recovery of a periodic condition- a qualitative study of parents´ experiences of PFAPA syndrome

  2019cites this paper
• Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Adenitis (PFAPA) Syndrome

  2019cites this paper
• Clinical Approach to the Diagnosis of Autoinflammatory Diseases

  2019cites this paper
• Periodic Fever, Aphthous Stomatitis, Pharyngitis, and Cervical Adenitis (PFAPA) Syndrome

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• Pediatric Oral Medicine

  2019cites this paper
• Periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis (PFAPA) syndrome: main features and an algorithm for clinical practice

  2019cites this paper
• Periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis syndrome - PFAPA syndrome.

  2019cites this paper
• The role of tonsillectomy in the Periodic Fever, Aphthous stomatitis, Pharyngitis and cervical Adenitis syndrome; a literature review

  2018cites this paper
• Unique histologic features of tonsils from patients with periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis (PFAPA) syndrome

  2018cites this paper
• PFAPA Syndrome in a Population with Endemic Familial Mediterranean Fever

  2018cites this paper
• Familial Mediterranean fever and periodic fever, aphthous stomatitis, pharyngitis, and adenitis (PFAPA) syndrome: shared features and main differences

  2018cites this paper
• An Underlooked Cause of Periodic Fever (PFAPA) in an Adult Patient with No Response to Tonsillectomy

  2018cites this paper
• Etiology and outcome of PFAPA (periodic fever, aphthous stomatitis, pharyngitis and adenitis) syndrome among patients operated with tonsillectomy in childhood

  2018cites this paper
• Health-related quality of life in children with PFAPA syndrome

  2018cites this paper
• The First International Conference on Periodic Fever, Aphthous Stomatitis, Pharyngitis, Adenitis Syndrome

  2017cites this paper
• Tonsillectomy as Treatment for Periodic Fever, Aphthous Stomatitis, Pharyngitis, and Cervical Adenitis Syndrome

  2017cites this paper
• Characteristics and Disease Course in a Cohort of Children With PFAPA Syndrome in the Community of Madrid, Spain.

  2017cites this paper
• Approach to recurrent fever in childhood.

  2017cites this paper
• [Tonsillectomy in Cases with Periodic Fever, Aphthous Stomatitis, Pharyngitis, and Cervical Adenitis Syndrome].

  2017cites this paper
• Familial Mediterranean fever with P369S/R408Q exon3 variant in pyrin presenting as symptoms of PFAPA

  2017cites this paper
• Long-Term Outcome of Classic and Incomplete PFAPA (Periodic Fever, Aphthous Stomatitis, Pharyngitis, and Adenitis) Syndrome after Tonsillectomy.

  2016cites this paper
• Response to cimetidine in a 1-year-old child with PFAPA syndrome.

  2016cites this paper
• PFAPA syndrome and Behçet’s disease: a comparison of two medical entities based on the clinical interviews performed by three different specialists

  2016cites this paper
• Tonsillar microbiota in children with PFAPA (periodic fever, aphthous stomatitis, pharyngitis, and adenitis) syndrome

  2016cites this paper
• Review of autoinflammatory diseases, with a special focus on periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis syndrome

  2016cites this paper
• Periodic Fever, Aphthous Stomatitis, Pharyngitis, and Cervical Adenitis (PFAPA) Syndrome: a Review of the Pathogenesis

  2016cites this paper
• Indications for tonsillectomy stratified by the level of evidence

  2016cites this paper
• Family History in Periodic Fever, Aphthous Stomatitis, Pharyngitis, Adenitis (PFAPA) Syndrome

  2016cites this paper
• Evidenz basierte Indikationen der Tonsillektomie

  2016cites this paper
• Is colchicine an effective treatment in periodic fever, aphtous stomatitis, pharyngitis, cervical adenitis (PFAPA) syndrome?

  2016cites this paper
• Lights and shadows in autoinflammatory syndromes from the childhood and adulthood perspective

  2016cites this paper
• Characterization of Variant Periodic Fever Phenotypes

  2016cites this paper
• Fever tree revisited: From malaria to autoinflammatory diseases.

  2015cites this paper
• Microbes of the tonsils in PFAPA (Periodic Fever, Aphtous stomatitis, Pharyngitis and Adenitis) syndrome – a possible trigger of febrile episodes

  2015cites this paper
• The Enigma of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Adenitis Syndrome

  2014cites this paper
• Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Adenitis (PFAPA) Syndrome in Iranian Children First Report of Iranian Periodic Fever and Autoinflammatory Registry (IPFAIR)

  2014cites this paper
• The labyrinth of autoinflammatory disorders: a snapshot on the activity of a third-level center in Italy

  2014cites this paper
• International periodic fever, aphthous stomatitis, pharyngitis, cervical adenitis syndrome cohort: description of distinct phenotypes in 301 patients.

  2014cites this paper
• The mean platelet volume levels in children with PFAPA syndrome.

  2014cites this paper
• PFAPA syndrome in adults.

  2014cites this paper
• Tonsillectomy for periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis syndrome (PFAPA).

  2014cites this paper
• Vitamin D levels and effects of vitamin D replacement in children with periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis (PFAPA) syndrome.

  2014cites this paper
• Familial Mediterranean fever in heterozygotes: are we able to accurately diagnose the disease in very young children?

  2013cites this paper
• A case of adult periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis (PFAPA) syndrome associated with endocapillary proliferative glomerulonephritis

  2013cites this paper
• Is PFAPA syndrome really a sporadic disorder or is it genetic?

  2013cites this paper
• A Taste of Periodic Fever Syndromes

  2013cites this paper
• Childhood versus adulthood-onset autoinflammatory disorders: myths and truths intertwined.

  2013cites this paper
• PFAPA syndrome: clinical characteristics and treatment outcomes in a large single-centre cohort.

  2013cites this paper
• Caution Should be Used in the Recognition of Adult-Onset Autoinflammatory Disorders: Facts or Fiction?

  2013cites this paper
• Maladies auto-inflammatoires chez l’enfant

  2013cites this paper
• A case of resistant adult-onset periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis (PFAPA) syndrome responsive to anakinra.

  2012cites this paper
• Periodic fever associated with aphthous stomatitis, pharyngitis and cervical adenitis.

  2012cites this paper
• Periodisches Fieber, aphthöse Stomatitis, Pharyngitis und Lymphadenitis (PFAPA-Syndrom) im Erwachsenenalter

  2012cites this paper
• Tonsillectomy in children with periodic fever with aphthous stomatitis, pharyngitis, and adenitis syndrome.

  2011cites this paper
• Nutzen und Wertigkeit der Adeno-Tonsillektomie bei Kindern und Jugendlichen mit PFAPA-Syndrom

  2011cites this paper
• PFAPA syndrome in a young adult with a history of tonsillectomy.

  2011cites this paper
• [Periodic fever, aphthous stomatitis, pharyngitis and adenitis: PFAPA syndrome in Argentina].

  2011cites this paper
• PFAPA syndrome in siblings. Is there a genetic background?

  2011cites this paper
• Long-Term Clinical Profile of Children With the Low-Penetrance R92Q Mutation of the TNFRSF1A Gene

  2011cites this paper
• [Consensus Document on the differential diagnosis and therapeutic approach to recurrent fever by the Paediatric Infectology Society and the Paediatric Rheumatology Society].

  2011cites this paper
• [Periodic fever, aphthous stomatitis, pharyngitis and adenitis syndrome].

  2011cites this paper
• The Eurofever Project: towards better care for autoinflammatory diseases

  2011cites this paper
• Urban legends: recurrent aphthous stomatitis.

  2011cites this paper
• Long-term follow-up of children with periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis syndrome.

  2011cites this paper
• Febrile recurrent respiratory infections or PFAPA syndrome: where is the bias?

  2011cites this paper
• Periodic Fever syndromes.

  2011cites this paper
• Periodic fever, apthous stomatitis, pharyngitis and adenitis syndrome

  2010cites this paper