Rescuing protein conformation: prospects for pharmacological therapy in cystic fibrosis.

No abstract is available for this paper.

• Publication year

  2002

• Venue

  Journal of Clinical Investigation

• Publication date

  2002-12-01

• Fields of study

  Biology, Medicine

• Identifiers
  DOI 10.1172/JCI16786PMID 12464661PMCID PMC151638
• External record

  Open on Semantic Scholar

• Source metadata

  Semantic Scholar, PubMed

• No claims are published for this paper.

• No concepts are published for this paper.

• Orchestrating the unfolded protein response in health and disease.

  2002cited by this paper
• Calcium-pump inhibitors induce functional surface expression of ΔF508-CFTR protein in cystic fibrosis epithelial cells

  2002cited by this paper
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  2001cited by this paper
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  2001cited by this paper
• Pharmacological treatment of the ion transport defect in cystic fibrosis

  2001cited by this paper
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• Induction of HSP 70 promotes D F 508 CFTR trafficking

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• The Delta F508 mutation shortens the biochemical half-life of plasma membrane CFTR in polarized epithelial cells.

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• Unraveling the roles of endoplasmic reticulum-associated degradation in metabolic disorders

  2023cites this paper
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