Nonpulmonary Manifestations of Cystic Fibrosis

Abstract While lung disease continues to be the main cause of morbidity and mortality, the improved survival rates have meant that nonpulmonary complications have become increasingly important in the care of individuals with cystic fibrosis. In this chapter, the gastrointestinal manifestations and other extrapulmonary aspects of cystic fibrosis are discussed. The topics covered include pancreatic disease, both pancreatic insufficiency and pancreatitis, hepatobiliary disease, fibrosing colonopathy, meconium ileus equivalent, and constipation. GI cancers and nutrition are also reviewed. There are brief discussions of infertility and diabetes mellitus in cystic fibrosis. For each of the major topics, the etiology, pathophysiology, clinical manifestations, and treatment are reviewed.

• Publication year

  2019

• Venue

  Kendig's Disorders of the Respiratory Tract in Children

• Publication date

  Unknown publication date

• Fields of study

  Medicine

• Identifiers
  DOI 10.1016/B978-0-323-44887-1.00052-3
• External record

  Open on Semantic Scholar

• Source metadata

  Semantic Scholar

• No claims are published for this paper.

• No concepts are published for this paper.

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