Partial remission with cyclosporine A in a patient with nephrotic syndrome due to NPHS2 mutation

No abstract is available for this paper.

• Publication year

  2009

• Venue

  Pediatric nephrology (Berlin, West)

• Publication date

  2009-06-03

• Fields of study

  Medicine

• Identifiers
  DOI 10.1007/s00467-009-1211-0PMID 19495806
• External record

  Open on Semantic Scholar

• Source metadata

  Semantic Scholar, PubMed

• No claims are published for this paper.

• No concepts are published for this paper.

• The actin cytoskeleton of kidney podocytes is a direct target of the antiproteinuric effect of cyclosporine A

  2008cited by this paper
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• Cyclosporin therapy in patients with Alport syndrome

  2007cited by this paper
• Steroid-resistant idiopathic childhood nephrosis: overdiagnosed and undertreated.

  2007cited by this paper
• Nephrotic Syndrome in the First Year of Life: Two Thirds of Cases Are Caused by Mutations in 4 Genes (NPHS1, NPHS2, WT1, and LAMB2)

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• Interventions for idiopathic steroid-resistant nephrotic syndrome in children.

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• Impact of Cyclosporin on Podocyte ZO-1 Expression in Puromycin Aminonucleoside Nephrosis Rats

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• Interventions for idiopathic steroid-resistant nephrotic syndrome in children.

  2004cited by this paper
• Patients with mutations in NPHS2 (podocin) do not respond to standard steroid treatment of nephrotic syndrome.

  2004influential reference
• Cyclosporine a slows the progressive renal disease of alport syndrome (X-linked hereditary nephritis): results from a canine model.

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• Long-term effects of cyclosporine A in Alport's syndrome.

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