Mammalian animal models for Duchenne muscular dystrophy.

No abstract is available for this paper.

• Publication year

  2009

• Venue

  Neuromuscular Disorders

• Publication date

  2009-04-01

• Fields of study

  Biology, Medicine

• Identifiers
  DOI 10.1016/j.nmd.2008.11.015PMID 19217290
• External record

  Open on Semantic Scholar

• Source metadata

  Semantic Scholar, PubMed

• No claims are published for this paper.

• No concepts are published for this paper.

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  2008cited by this paper
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• Long-term blinded placebo-controlled study of SNT-MC17/idebenone in the dystrophin deficient mdx mouse: cardiac protection and improved exercise performance

  2008cited by this paper
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  2008cited by this paper
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  2007cited by this paper
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  2006cited by this paper
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  2005cited by this paper
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  2005cited by this paper
• Molecular Pathogenesis of Genetic and Inherited Diseases A Multidisciplinary Evaluation of the Effectiveness of Cyclosporine A in Dystrophic Mdx Mice

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  2004cited by this paper
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• Enhanced Expression of the α7β1 Integrin Reduces Muscular Dystrophy and Restores Viability in Dystrophic Mice

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• Elevated subsarcolemmal Ca 2 1 in mdx mouse skeletal muscle fibers detected with Ca 2 1 -activated K 1 channels

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• Role for α-Dystrobrevin in the Pathogenesis of Dystrophin-Dependent Muscular Dystrophies

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• Decreased myocardial nNOS, increased iNOS and abnormal ECGs in mouse models of Duchenne muscular dystrophy.

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• New mdx mutation disrupts expression of muscle and nonmuscle isoforms of dystrophin

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  1992cited by this paper
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  1992cited by this paper
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• Changes to the Autophagy-Related Muscle Proteome Following Short-Term Treatment with Ectoine in the Duchenne Muscular Dystrophy Mouse Model mdx

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• Severe cardiac and skeletal manifestations in DMD-edited microminipigs: an advanced surrogate for Duchenne muscular dystrophy

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• The Use of Collagen Methacrylate in Actuating Polyethylene Glycol Diacrylate–Acrylic Acid Scaffolds for Muscle Regeneration

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• Acute toxicity and regenerative dose finding of an extract of Miconia ferruginata DC. in a mouse model of Duchenne muscular dystrophy.

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• Treino de baixa intensidade mantem a funcionalidade e fibrose em camundongos mdx

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• Beneficial Effect of H2S-Releasing Molecules in an In Vitro Model of Sarcopenia: Relevance of Glucoraphanin

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• Current Pharmacological Strategies for Duchenne Muscular Dystrophy

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• Muscle spindle function in healthy and diseased muscle

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• Influence of botulinum toxin A on craniofacial morphology after injection into the right masseter muscle of dystrophin deficient (mdx-) mice.

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• De novo revertant fiber formation and therapy testing in a 3D culture model of Duchenne muscular dystrophy skeletal muscle.

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• The microRNA, miR-133b, functions to slow Duchenne muscular dystrophy pathogenesis

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• Safety issues and harmful pharmacological interactions of nutritional supplements in Duchenne muscular dystrophy: considerations for Standard of Care and emerging virus outbreaks

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• X-linked muscular dystrophy in a Labrador Retriever strain: phenotypic and molecular characterisation

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• Dystrophin Is Required for the Proper Timing in Retinal Histogenesis: A Thorough Investigation on the mdx Mouse Model of Duchenne Muscular Dystrophy

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• Dystrophic Dmdmdx rats show early neuronal changes (increased S100β and Tau5) at 8 months, supporting severe dystropathology in this rodent model of Duchenne Muscular Dystrophy.

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• Phylogeny can Inform Animal Model Development for Both Inherited and Induced Conditions: Duchenne’s Muscular Dystrophy (DMD) and Fetal Alcohol Spectrum Disorders (FASD)

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• X-linked muscular dystrophy in a Labrador Retriever strain: phenotypic and molecular characterization.

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